Phenylketonuria

This site named "PKU Diet" is designed for parents of children with one of inherited diseases, leading to intolerance of one amino acid - phenylalanine. This disease called phenylketonuria (PKU). Despite significant advances made by scientists in understanding the mechanisms of development and methods of medicinal treatment of this disease, including enzyme and cofaktor therapy, the primary and still an effective treatment for PKU is the diet, developed over 50 years ago .

Diet
Features
Requirements for equipment
Register
Using this site
Main Menu
Selection of products
Selection of recipes

Diet

The basis of therapeutic diets is artificially synthesized substitutes protein without toxic to a child amino acids - phenylalanine. The remaining components of food such as fats, carbohydrates, vitamins and minerals may be added to such a substitute in production (which is often done for children of the first year of life), or enter the body from normal food.

The main challenge in compiling a list of products is to provide the child's growth and development, giving all components of food, avoiding excess phenylalanine. Therefore, at diet drawing up it is necessary to consider set of the interconnected factors - amino acid composition of proteins, the amount of other nutrients, as well as the overall calorie content of food. The point is that if the body lacks the energy from carbohydrates and fats, it starts to get it out of the body's own proteins, that contain a significant amount of phenylalanine. This often happens, at the raised physical activities at children, diseases with increased body temperature and even at a teething. Besides, it is desirable to achieve an adequate income other amino acid, which is usually not enough for children with PKU - tyrosine. The deficit of tyrosine happen due to the fact that it is usually synthesized in the body from phenylalanine, but in PKU children this process is broken..

Top

Features

Using the software of our site you will be able to solve several problems:

Top

Equipment required

To access the site, you may use a mobile phone with support WAP access to the Internet (it is almost any modern phone) or Communicator or a computer with Internet access.

top

Registration

To ensure privacy of your data , registration is required.

Using the site

top

Main menu.

All pages have, "PKU Diet" button. Click on this button brings you to the main website menu. It consists of the following items::

  1. Current day view window with the result of calculation to date, as well as functions for adding and changing set of products and ready meals for today;
  2. Inspection the registration of current data on growth, weight, and portability of phenylalanine (in mg per kg of body weight), also indicates kind of protein substitute;
  3. Information about the child it is necessary to specify the sex, date of birth and the beginning of treatment (these data are needed to calculate the menu), you can also specify the passport data (name of child) and country (region) of residence;
  4. Products - This mode allows you to view the nutritional value of food in the database (about 300 titles), including the contents of the main amino acids;
  5. Recipes -here you can create, view, correct (the recipes are created by you), ready meals, consisting of products used in the program;
  6. Help you are currently reading;
  7. Feedback if you want to send a message to the authors of the program;
  8. Exit ends the session, allows change the user.
top

Selection of products

In this mode you can view a list of products, to choose necessary and to calculate their quantity taking into account child’s phenylalanine tolerance.

top

Selection of recipes

In this mode you can use the recipes (the lists of products), created by you or other visitors of the site, select the necessary and enter them with automatic calculation of phenylalanine.

In addition from the view the examination you can access to the archive of inspections, from the view of products - view the sets of products over the past few days and from the view of sets of recipes - view an archive of recipes used.

Main menu